| Foreword | 6 |
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| Preface | 7 |
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| Contents | 8 |
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| I Malignant Cutaneous Neoplasms | 11 |
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| Angiosarcoma | 12 |
| Cutaneous B- Cell Lymphoma | 17 |
| Granulomatous Slack Skin | 24 |
| Langerhans Cell Histiocytosis | 28 |
| Leukemia Cutis | 33 |
| Mast Cell Disease ( Urticaria Pigmentosa) | 36 |
| Merkel Cell Carcinoma | 41 |
| Metastatic Carcinoma | 47 |
| Paget’s Disease | 52 |
| Subcutaneous Panniculitis- like Lymphoma | 56 |
| II Hereditary Cancer- Predisposition Syndromes and Paraneoplastic Disorders | 60 |
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| Muir- Torre Syndrome | 61 |
| Acquired Ichthyosis, Acanthosis Nigricans, Palmar Hyperkeratosis | 67 |
| Amyloidosis: Systemic, Nodular, and Epidermal Derived | 72 |
| Birt- Hogg- Dubé Syndrome | 77 |
| Cowden’s Syndrome | 82 |
| Gyrate Erythemas: Erythema Gyratum Repens and Erythema Chronicum Migrans | 87 |
| Gardner Syndrome | 92 |
| Multicentric Reticulohistiocytosis | 97 |
| Multiple Cutaneous Leiomyomas | 101 |
| Lethal Non- Langerhans Cell Histiocytoses: Necrobiotic Xanthogranuloma and Xanthoma Disseminatum | 104 |
| Pancreatic Panniculitis | 109 |
| Scleromyxedema | 112 |
| Necrolytic Migratory Erythema | 116 |
| III Infectious Diseases | 120 |
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| Anthrax | 121 |
| Ecthyma Gangrenosum | 127 |
| Rocky Mountain Spotted Fever and the Rickettsioses | 131 |
| Smallpox | 135 |
| Staphylococcal Toxin- Mediated Scalded Skin and Toxic Shock Syndromes | 139 |
| Meningococcemia and Purpura Fulminans | 143 |
| IV Inborn Errors of Metabolism and Autoimmune Disease | 149 |
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| Lethal Hereditary Vascular Disorders: Osler- Weber- Rendu, Ataxia- Telangiectasia, and Fabry’s Disease | 150 |
| Eruptive Xanthoma | 155 |
| Graft- versus- Host Disease | 159 |
| Paraneoplastic Pemphigus and Pemphigus Vulgaris | 162 |
| Relapsing Polychondritis | 166 |
| Vascular Diseases | 170 |
| Calciphylaxis ( Calcific Uremic Arteriolopathy) | 171 |
| Kawasaki Disease | 177 |
| Polyarteritis Nodosa | 182 |
| Index | 187 |